Cuidados de enfermagem prestados aos pacientes portadores de hemofilia: uma revisão integrativa

Abstract

Hemophilia is a genetic and hereditary bleeding disorder linked to the X chromosome, which requires specific interventions. The objective of this study was to identify nursing practices that optimize the clinical management of these patients, improving care and outcomes. This is an integrative review that included qualitative studies published between 2014 and 2024, with searches in the BVS, PubMed, ScienceDirect and CINAHL databases, the selection was guided by the PRISMA method. The results indicated the relevance of the nurse as the first point of contact and link between patients, family members and the health system, playing an essential role in education and health promotion. The use of Nursing Care Systematization (NCS) was indicated as a fundamental tool to individualize care and ensure adherence to treatment, promoting autonomy and preventing complications. However, the lack of specific studies and the need for continuous training to fill gaps related to the knowledge of health professionals about the management of hemophiliac patients stand out. Thus, it is clear that SAE, combined with a holistic approach and specialized training, is essential to improve nursing care and actions in promoting the quality of life of patients with hemophilia. This research highlights the importance of expanding studies on nursing care for hemophilic patients, emphasizing the essential role of nurses in providing comprehensive and individualized care from initial contact through ongoing treatment.